Recurrent hemoptysis as a complication of cystic fibrosis. Implications for treatment
Hemoptisis recurrente como complicación de la fibrosis quística. Implicaciones para el tratamiento
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Hemoptysis is a commonly reported complication in patients with cystic fibrosis. It affects about 9% of the population. It can be of scarce quantity or massive (4%-5% of patients); the latter is defined as bleeding greater than 240 mL during a 24-hour period. Its pathogenesis is not completely understood, but the most commonly related cause is persistent inflammation of the airway associated with neovascularization, with tortuosity and damage of bronchial arteries, whose pressure values are systemic.
We describe the case of a young patient with confirmed cystic fibrosis in whom hemoptysis was successfully controlled with a stepwise treatment of the complication.
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