Pleuropulmonary synovial sarcoma: report of an unusual entity in a Peruvian hospital
Sarcoma sinovial pleuropulmonar: reporte de una entidad inusual en un hospital peruano
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Primary pulmonary synovial sarcoma (SS) is a tumor derived from pluripotential mesenchymal cells. It accounts for 0.1-0.5% of all pulmonary tumors and typically occurs in young, non-smoking individuals, classified according to the cellular pattern as monophasic or biphasic. Intrathoracic involvement can occur in various locations, including the pleuropulmonary region, mediastinum, thoracic wall, trachea, and diaphragm. Diagnosis is challenging and treatment includes surgery, chemotherapy, and radiotherapy. We present the case of a 65-year-old male patient with no smoking history who was admitted due to progressive dyspnea, chest pain, and weight loss. Thoracic computed tomography revealed moderate pleural effusion associated with a heterogeneous mass in the left hemithorax. Histopathology of the tissue obtained by percutaneous biopsy reported a primarily monophasic synovial sarcoma. Palliative treatment with serial pleural drainage, chemical pleurodesis, and pain management was indicated. The patient passed away 10 months after the onset of symptoms.
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